2.5 year-old female child presents with abnormal auricle

 

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Doctor's Information

Name : Seyed Morteza
Family :Bagheri
Affiliation : Radiology Department,Hasheminejad Hospital,TUMS
Academic Degree: Assistant Professor of Radiology
Email : This email address is being protected from spambots. You need JavaScript enabled to view it.
Resident : Mehdi Aghdasi

 

Patient's Information

Gender : Female
Age : 2

 

Case Section

Head & Neck Imaging

 

Clinical Summary

A 2.5 year female child presents with abnormal auricle

 

 

Imaging Procedures and Findings

Axial CT scan sections at the level of temporal bone : In right side the EAC is completely atretic ,the structures of the middle ear are not seen and the basal turn of cochlea is deformed. Effusion in left middle ear is noted. Ethmoidal sinusitis is also present.

 

Discussion

Malformations of the outer ear are referred to as congenital aural dysplasias (CAD). A malformation of the auricle alone is referred to as microtia . CAD has been estimated to occur in 1 of 3300 to 10,000 births, with a higher incidence of 1 in 900 reported in the era of thalidomide embryopathy . CAD is most commonly isolated, without known cause, and unilateral. The right ear is more commonly affected, and in up to one third of cases, CAD may be bilateral. CAD may also occur in conjunction with other organ abnormalities due to genetic disorders, chromosomal aberrations, intrauterine infections, and environmental Teratogens. Middle ear abnormalities tend to occur concomitantly with CAD because of the common embryologic origins of the EAC and middle ear. Pneumatization of the middle ear cavity is often reduced in CAD, with the extent of reduction correlating directly with the severity of the dysplasia. Although pneumatization of the entire middle ear can be affected, the hypotympanumis usually most severely reduced.

 

Final Diagnosis

Complex congenital anomaly of right temporal bone

 

References

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